Fuchs' heterochromic uveitis associated with retinitis pigmentosa in a father and son.

of oculomotor and trochlear nerve involvement have also been reported.' With intracranial hypertension, changes in seventh nerve function are exceptional. Peripheral facial nerve palsy was observed in five individuals suffering from benign intracranial hypertension.78 In one additional patient facial myokymia has been observed, thus showing that, with intracranial hypertension, facial nerve involvement can result in axonal hyperactivity. No clear explanation was offered as to the pathophysiology of the facial nerve involvement in intracranial hypertension, although it was felt that this dysfunction represented a non-specific pressure related phenomenon. In our patient, it is conceivable that the displacement of intracranial nervous structures related to the ArnoldChiari type I malformation played a role in the mechanism of this peculiar eyelid phenomenon, by allowing the seventh cranial nerve to be affected by elevation in intracranial pressure.